Computer tomographic semiotics of retroperitoneal leiomyosarcoma arising from the muscular wall of the splenic vein: a case report
https://doi.org/10.21294/1814-4861-2018-17-6-123-127
Abstract
Background. Diagnostic imaging of retroperitoneal neoplasms that arise within the retroperitoneal space but outside the major organs in this space is challenging due to the presence of large spaces filled with fatty tissue that allows the tumor to develop asymptomatically for a long time. In addition, these tumors are rare, and radiological semiotics and clinical manifestations can be nonspecific.
Case presentation. We present the rare clinical case of a 53-year-old patient with a large retroperitoneal mass detected by contrast-enhanced computed tomography. Additional imaging diagnostic procedures as well as histological findings helped to make a definitive diagnosis: extraorganic retroperitoneal leiomyosarcoma arising from the muscular wall of the splenic vein.
Conclusion. The retrospective analysis of CT data showed that the tumor-induced marginal defect in the contrasted splenic vein may indicate the tumor arising from the muscular wall of the vessel. The final diagnosis was made on the basis of a morphological study.
About the Authors
I. D. Lagkueva
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Irina D. Lagkueva - MD, Researcher, Department of New Technologies and Semiotics of Radiological Diagnosis of Diseases of Organs and Systems.
86, Profsoyuznaya Street, 117997-Moscow
V. A. Rebrikova
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Vera A. Rebrikova - MD, Researcher, Department of New Technologies and Semiotics of Radiological Diagnosis of Diseases of Organs and Systems.
86, Profsoyuznaya Street, 117997-Moscow
E. V. Egorova
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Ekaterina V. Egorova - MD, PhD, Senior Researcher, Department of New Technologies and Semiotics of Radiological Diagnosis of Diseases of Organs and Systems.
86, Profsoyuznaya Street, 117997-Moscow
N. L. Sergeev
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Nikolai I. Sergeev - MD, PhD, Leading Researcher, Department of New Technologies and Semiotics of Radiological Diagnosis of Diseases of Organs and Systems.
86, Profsoyuznaya Street, 117997-Moscow
P. M. Kotlyarov
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Pyotr M. Kotlyarov - MD, Professor, Head of the Department of New Technologies and Semiotics of Radiological Diagnosis of Diseases of Organs and Systems.
86, Profsoyuznaya Street, 117997-Moscow
O. P. Bliznyukov
Russian Scientific Center of Roentgenoradiology of the Ministry of Healthcare of the Russian Federation
Russian Federation
Russian Federation
Oleg P. Bliznyukov - MD, DSc, Head of the Pathoanatomical Department.
86, Profsoyuznaya Street, 117997-Moscow
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Review
For citations:
Lagkueva I.D., Rebrikova V.A., Egorova E.V., Sergeev N.L., Kotlyarov P.M., Bliznyukov O.P. Computer tomographic semiotics of retroperitoneal leiomyosarcoma arising from the muscular wall of the splenic vein: a case report. Siberian journal of oncology. 2018;17(6):123-127. (In Russ.) https://doi.org/10.21294/1814-4861-2018-17-6-123-127
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